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Short tutorial. Treatment options in light chain amyloidosis and monoclonal gammopathy of renal significance

Short tutorial. Treatment options in light chain amyloidosis and monoclonal gammopathy of renal significance

Source : https://link.springer.com/article/10.1007/s12254-021-00689-2

AL amyloidosis (AL) and monoclonal gammopathy of renal significance (MGRS) are both paraprotein-associated diseases. Both entities are based on a monoclonal paraprotein produced by a clonal plasma-cell population like in monoclonal gammopathy of undetermined significance (MGUS) or by a B-cell population like in low grade lymphoma.